ʻO ka paʻi hou loa o ka World Health Organization's Classification of Soft Tissue and Bone Tumors, i paʻi ʻia ma ʻApelila 2020, e hoʻokaʻawale ananā sarcomai ʻekolu mau māhele: snā puʻupuʻu ʻiʻo pinepine, nā puʻupuʻu iwi, a me nā puʻupuʻu o ka iwi a me nā ʻiʻo palupalu me nā pūnaewele poepoe liʻiliʻi i hoʻokaʻawale ʻole ʻia(e like me ka EWSR1-non-ETS fusion round cell sarcoma).
"ʻO ke Kanesa i Poina"
He ʻano maʻamau ʻole ʻo Sarcomaka maʻi ʻaʻai i nā pākeke, e helu ana no kahi1%o nā maʻi kanesa makua āpau, i kapa pinepine ʻia ʻo "The Forgotten Cancer." Eia nō naʻe, he mea pili iamea maʻamau i nā keiki, e helu ana no a puni15% a i 20%o nā maʻi ʻaʻai kamaliʻi āpau. Hiki ke loaʻa i kēlā me kēia ʻāpana o ke kino, ʻo ka mea maʻamau i loko o kanā lima a i ʻole nā wāwae(60%), ukali ʻia e kakino a ʻōpū paha(30%), a ʻo ka hope loapoʻo a ʻāʻī paha(10%).
I nā makahiki i hala iho nei, ua piʻi mālie ka nui o nā puʻupuʻu iwi a me nā ʻiʻo palupalu. ʻOi aku ka maʻamau o nā puʻupuʻu iwi malignant mua i nā ʻōpio a me nā poʻe waena a me ka osteosarcoma, Ewing sarcoma, chondrosarcoma, malignant fibrous histiocytoma, a me chordoma, a me nā mea ʻē aʻe. ʻO nā puʻupuʻu ʻiʻo palupalu maʻamau e komo pū me ka synovial sarcoma, fibrosarcoma, liposarcoma, a me rhabdomyosarcoma. ʻOi aku ka maʻamau o nā metastases iwi i nā poʻe waena a me ka poʻe ʻelemakule, me nā puʻupuʻu mua maʻamau he maʻi kanesa māmā, ka maʻi kanesa umauma, ka maʻi kanesa puʻupaʻa, ka maʻi kanesa prostate, a me ka maʻi kanesa thyroid, a me nā mea ʻē aʻe.
Ka ʻIke Mua, Ka Lāʻau Mua - Ke Hoʻomālamalama nei i nā "Tumors" i Huna ʻia
Ma muli o ke kiʻekiʻe o ka hoʻi hou ʻana o nā sarcomas, he nui nā puʻupuʻu i loaʻa nā hōʻailona ma mua o ke ʻoki ʻana a nele i nā hoʻokolohua kiʻi kikoʻī. ʻO kēia ke alakaʻi pinepine i ka ʻike ʻana i ka wā o ke ʻoki ʻana ʻaʻole maʻalahi ka puʻupuʻu e like me ka mea i manaʻo ʻia ma mua o ke ʻoki ʻana, e hopena ana i ka hemo ʻole ʻana. Hiki ke hana hou ʻia a i ʻole ka metastasis ma hope o ke ʻoki ʻana, e hoʻolilo ana i nā mea maʻi i ka manawa kūpono e mālama ai. No laila,ʻo ka ʻike mua ʻana, ka hōʻoia pololei, a me ka mālama ʻana i ka manawa kūpono he hopena koʻikoʻi nui ia i ka prognosis o nā maʻi. I kēia lā, makemake mākou e hoʻolauna i kahi loea hanohano nona ka ʻike ma kahi o 20 mau makahikii ka hōʻoia maʻamau a me ka mālama pilikino o ka sarcoma palupalu, a ua mahalo nui ʻia e ka ʻoihana a me nā mea maʻi -KaukaLiu Jiayongmai ke Keʻena o ka Iwi a me nā ʻiʻo palupalu ma ka Halemai Kanesa o ke Kulanui ʻo Peking.
Ke wehe nei i ka loea me ka ʻike hohonu o ka ʻeha iwi a me ke kino - Kauka.Liu Jiayong
Kauka Lapaʻau, Kauka Nui, Polopeka Hoa. Ua aʻo ʻia ma ke Kikowaena Kanesa Anderson ma ʻAmelika Hui Pū ʻIa.
ʻIke loea:ʻO ka mālama piha ʻana i nā sarcomas palupalu o nā ʻiʻo (ʻoki ʻoki a me ke kūkulu hou ʻana; chemotherapy, lāʻau lapaʻau i hoʻopaʻa ʻia, a me ka immunotherapy); mālama ʻoki kino o nā melanomas.
Me kahi kokoke i 20 mau makahiki o ka ʻike lapaʻau, ua hōʻiliʻili ʻo Kauka Liu Jiayong i ka ʻike loea lapaʻau a me ke ʻoki kino nui manā hoʻolālā hōʻoia maʻamau a me nā hoʻolālā lapaʻau pilikinono nā sarcomas palupalu maʻamau e like me ka undifferentiated pleomorphic sarcoma, liposarcoma, leiomyosarcoma, synovial sarcoma, adenocystic carcinoma-like sarcoma, epithelioid sarcoma, fibrosarcoma, angiosarcoma, a me infiltrative fibromatosis. ʻO ia ke ʻano kūikawāakamai i ka lawelawe ʻana i nā kīʻaha koko a me nā aʻalolo i ka wā o ka ʻoki ʻana i ka sarcoma limb, a me ka hoʻoponopono ʻana a me ke kūkulu hou ʻana i nā kīnā palupalu ma ka ʻili.Hoʻolohe mālie ʻo Kauka Liu i kēlā me kēia maʻi, nīnau pono e pili ana i kā lākou mōʻaukala lapaʻau, a lawe i nā moʻolelo lapaʻau kikoʻī. Hoʻolohe nui ʻo ia i nā loli o ke kūlana o ka mea maʻi i nā manawa like ʻole, e like me ma mua a ma hope o ke ʻoki ʻana, i ka wā o ka mālama ʻana, ka hahai ʻana, a me ka holomua o ka maʻi, e hana ana i nā hoʻoholo pololei a me ka hoʻoponopono kūpono i nā hoʻolālā lapaʻau.
I kēia manawa, lawelawe ʻo Kauka Liu Jiayong ma ke ʻano he lālā o ka Soft Tissue Sarcoma and Melanoma Group o ka Chinese Anti-Cancer Association, a he lālā hoʻi o ka Bone Tumor Group o ka Beijing Society of Orthopedics of the Chinese Medical Association.I ka makahiki 2010, ʻo ia ka mea mua ma Kina e unuhi a hoʻopuka i ka "NCCN Clinical Practice Guidelines in Soft Tissue Sarcoma," e paipai ana i ka mālama piha maʻamau o nā sarcomas palupalu.Ke hoʻomau nei ʻo ia i ka hoʻoikaika no ka holomua i ka noiʻi lapaʻau a me ka ʻepekema, ʻoiai he nui ka ukana o nā mea maʻi. Ua hoʻolaʻa ʻia a kuleana ʻo ia no kēlā me kēia mea maʻi āna e mālama ai, a i ka wā o ke ahulau, ua hoʻoponopono ʻo ia i nā pilikia i kū i nā mea maʻi e ʻimi nei i ka mālama olakino ma o ka pane koke ʻana i nā kūkākūkā a nā mea maʻi, ka nānā ʻana i nā hopena hahai, a me ka hāʻawi ʻana i nā ʻōlelo aʻoaʻo lapaʻau kūpono ma o nā kahua kūkākūkā pūnaewele e like me Good Doctor's Patient Group.
Hihia Hou
ʻO Mr. Zhang, he maʻi 35 makahiki, ua nalowale koke kona ʻike i ka hoʻomaka ʻana o 2019. Ma hope mai, ua hana ʻia ʻo ia i ke ʻoki enucleation maka hema ma muli o ka hoʻonui mau ʻana o ke kaomi intraocular. Ua hōʻike ka pathology postoperative i kahi pseudotumor inflammatory. I ke kauwela o ia makahiki hoʻokahi, ua loaʻa nā nodules māmā he nui i ka wā o ka hoʻokolokolo ʻana, akā ʻaʻohe cell tumor i ʻike ʻia ma o nā biopsies nila. Ua hōʻike nā hoʻokolokolo hahai hou aku i nā metastases iwi a me ka māmā he nui. Ua ʻike ʻia ʻo ia e nā kūkākūkā ma nā haukapila kūloko a me nā haukapila kiʻekiʻe me ka tumor myofibroblastic inflammatory. I ʻAukake 2022, ua hana ʻia ʻo ia i ka chemotherapy kiʻekiʻe, kahi i hōʻoluʻolu nui i kona ʻeha akā ʻaʻole i hōʻike i ka hoʻomaikaʻi ʻana i nā lesions ma hope o ka loiloi hou ʻana. Ua nāwaliwali hoʻi kona kūlana kino. ʻOiai me kēia, ʻaʻole i haʻalele kona ʻohana i ka manaʻolana. Ma hope o ka ʻimi ʻana i nā manaʻo he nui, ua hele mai lākou i ka nānā ʻana o Kauka Liu Jiayong i Nowemapa 2022. Ma hope o ka nānā pono ʻana i ka mōʻaukala olakino o ka mea maʻi, nā moʻolelo olakino āpau, nā hoʻokolohua pathological, a me ka ʻikepili kiʻi,KaukaUa hāpai ʻo Liu i kahi papa hana chemotherapy e pili ana i ka methotrexate haʻahaʻa a me Changchun Ruibin.He kūpono ke kumukūʻai o kēia ʻano hana chemotherapy a he liʻiliʻi nā hopena ʻaoʻao. Ma hope o 35 mau lā o ka lāʻau lapaʻau, ua hōʻike kahi CT scan ma hope ua nalowale ka nui ma ka māmā ʻākau, e hōʻike ana i ka kaohi maikaʻi ʻana o ka puʻupuʻu.Ua hōʻike ʻia kahi hoʻokolohua ma hope koke iho nei ma ka Halemai ʻOncology o ka ʻĀpana Hema o Beijing i ke kūlana paʻa o ka māmā, a ua ʻōlelo ʻo Kauka Liu i nā kipa maʻamau. I kēia manawa, ua ʻoi aku ka hilinaʻi o ka mea maʻi a me kona ʻohana i ka mālama ʻana ma hope, piha i ka manaʻolana. Manaʻo lākou ua ʻike lākou i kahi kukui mālamalama i ka huakaʻi o ka mālama ʻana a hōʻike i ko lākou mahalo nui ma ka hōʻike ʻana i kahi hae silika o ka mahalo.
Ka manawa hoʻouna: ʻAukake-25-2023



